Rosai dorfman disease with haemolytic anaemia in an elderly patient: a rare presentation.
نویسندگان
چکیده
Rosai Dorfman disease (RDD) or sinus histiocytosis with massive lymphadenopathy (SHML) is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms.The authors report a 56 year old man who presented with massive generalised lymphadenopathy with haemolytic anaemia. Histopathological examination demonstrated lymphophagocytosis (emperipolesis) consistent with a diagnosis of RDD. Clinicians need to be aware of this entity which can present as a rare differential diagnosis of benign lymphoproliferative disorders.
منابع مشابه
Rosai-Dorfman Disease: A Case Report and Literature Review
Rosai-Dorfman disease or sinus histiocytosis with massive lymphadenopathy is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms whose etiology remains poorly elucidated. The diagnosis is based on immunohistochemistry. Its treatment is poorly defined but the prognosis is usually favorable. Here we report a 14 year old boy who presented with massive bilateral cervi...
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عنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 64 1 شماره
صفحات -
تاریخ انتشار 2016