Rosai dorfman disease with haemolytic anaemia in an elderly patient: a rare presentation.

نویسندگان

  • Harshit Jain
  • Nikhil Gupta
  • Jalees Fatima
  • Ritu Karoli
  • Vaibhav Shukla
چکیده

Rosai Dorfman disease (RDD) or sinus histiocytosis with massive lymphadenopathy (SHML) is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms.The authors report a 56 year old man who presented with massive generalised lymphadenopathy with haemolytic anaemia. Histopathological examination demonstrated lymphophagocytosis (emperipolesis) consistent with a diagnosis of RDD. Clinicians need to be aware of this entity which can present as a rare differential diagnosis of benign lymphoproliferative disorders.

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عنوان ژورنال:
  • The Journal of the Association of Physicians of India

دوره 64 1  شماره 

صفحات  -

تاریخ انتشار 2016